{"product_id":"recombinant-human-sco-cytochrome-oxidase-deficient-homolog-2-bhp11003203","title":"Recombinant Human SCO Cytochrome Oxidase Deficient Homolog 2","description":"\u003cp\u003e\u003cstrong\u003eRecombinant Human SCO Cytochrome Oxidase Deficient Homolog 2\u003c\/strong\u003e is supplied as a recombinant protein for in vitro research use.\u003c\/p\u003e\n\u003ch3\u003eBackground\u003c\/h3\u003e\n\u003cp\u003eSCO2 protein is a member of the SCO1\/2 family. SCO1 and SCO2 proteins are found on the inner membrane of the mitochondria and takes a vital part copper insertion or transport to the active site of cytochrome c oxidase (COX). Flaws in SCO2 are the reason for deadly infantile cardioencephalomyopathy with cytochrome c oxidase deficiency (FIC) which is characterized by hypertrophic cardiomyopathy, lactic acidosis, and gliosis. Heart and skeletal muscle display declines in cytochrome c oxidase (COX) activity, while liver and fibroblasts show mild COX deficiencies.\u003c\/p\u003e\n\u003ch3\u003eProduct format\u003c\/h3\u003e\n\u003cp\u003eProvided as a recombinant protein suitable for in vitro workflows such as binding studies, screening, and assay development. Refer to the specifications table for expression format and molecular properties.\u003c\/p\u003e","brand":"ProSpec-Tany TechnoGene Ltd","offers":[{"title":"2 ug","offer_id":53038104215917,"sku":"pro-054-2UG","price":60.0,"currency_code":"USD","in_stock":true},{"title":"10 ug","offer_id":53038391001453,"sku":"pro-054-10UG","price":145.0,"currency_code":"USD","in_stock":true},{"title":"1 mg","offer_id":53038391034221,"sku":"pro-054-1MG","price":5200.0,"currency_code":"USD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0949\/7424\/7277\/files\/Prospecbio-sco2-human-PRO-054.png?v=1782158245","url":"https:\/\/www.ebiohippo.com\/products\/recombinant-human-sco-cytochrome-oxidase-deficient-homolog-2-bhp11003203","provider":"BioHippo","version":"1.0","type":"link"}